Lumbar Intradural Extramedullary Isolated Hemagioblastoma: A Rare Entity and Review of Literature

Abstract

The terminology “Intradural Extramedullary” is often associated with Nerve sheath tumors (schwannoma, Neurofibroma) and Meningioma, while dermoid cyst, epidermoid, neurenteric cyst are other benign entities. Hemangioblastomas are rare, accounting for 1-5% of all spinal cord tumours.1 75% of the Spinal hemangiblastoma are Intramedullary, and another 10-15% have combined intramedullary and extramedullary-intradural component, while isolated extramedullary hemangioblastoma are rare1. Our case had an isolated intradural extramedullary hemangioblastoma without any associated manifestations of VHL syndrome. Surgery is a preferred option where total resection is possible, where as SRS is also an option in case of residual or incomplete resection.